TY - JOUR AU - Egido Turrión, Cristina AU - Rossi, Elisa AU - Ollauri Ibáñez, Claudia AU - Pérez García, María Luisa AU - Sevilla Toral, María Ángeles AU - Bastida Bermejo, José María AU - González Porras, José Ramón AU - Rodríguez Barbero, Alicia AU - Bernabeu, Carmelo AU - López-Novoa, José M. AU - Pericacho Bustos, Miguel PY - 2022 SN - 2296-858X UR - http://hdl.handle.net/10366/154602 AB - [EN] Hereditary Hemorrhagic Telangiectasia (HHT) is an autosomal-dominant genetic disorder involving defects in two predominant genes known as endoglin (ENG; HHT-1) and activin receptor-like kinase 1 (ACVRL1/ALK1; HHT-2). It is characterized by... LA - eng PB - Frontiers KW - Rendu-Osler Disease KW - Bleeding KW - ALK1 (ACVRL1) KW - Hereditary Hemorrhagic Telangiectasia (HHT) KW - Epistaxis KW - Hemostasia KW - Endoglin (CD105) KW - Epistaxis KW - Telangiectasia, Hereditary Hemorrhagic KW - Bleeding Time KW - Hemostasis TI - Functional Alterations Involved in Increased Bleeding in Hereditary Hemorrhagic Telangiectasia Mouse Models. DO - 10.3389/fmed.2022.871903 T2 - Frontiers in medicine VL - 9 M2 - 871903 ER -